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BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide, BCKDHB)

Short Description: Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform. [provided by RefSeq, Jul 2008].
More information related to gene BCKDHB.

Products related to BCKDHB Gene:

55 results :

Human BCKDHB ORF Clone in Cloning Vector
ORF Clon Cloning Vector pORF Spectinomycin unconjugated Transient
Type:
ORF
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Vector type:
Cloning Vector
Vector backbone:
pORF
Resistance Gene:
Spectinomycin
Expression:
Transient
Catalog No. ABIN5733141
Datasheet
Catalog No. ABIN5733141
Type:
ORF
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Insert length:
1179 bp
Vector type:
Cloning Vector
Vector backbone:
pORF
Resistance Gene:
Spectinomycin
Expression:
Transient
Sequencing Primer:
  • M13 FP: 5'-CCCAGTCACGACGTTGTAAAACG-3'
    M13 RP: 5'-CAGGAAACAGCTATGAC-3'
Format:
Liquid
Buffer:
10  mM Tris-HCI, 1  mM EDTA,  pH 8.0
Storage:
-20 °C
Human BCKDHB cDNA Clone in Mammalian Expression Vector (HA tag)
cDNA PExp Mammalian Expression Vector pPM-C-HA Kanamycin CMV Promoter HA tag Stable
Type:
cDNA
Application:
Protein Expression
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Vector type:
Mammalian Expression Vector
Vector backbone:
pPM-C-HA
Resistance Gene:
Kanamycin
Selection Marker:
Neomycin
Promoter:
CMV Promoter
Fusion Tag:
HA tag
Expression:
Stable, Transient
Catalog No. ABIN4472593
Datasheet
Catalog No. ABIN4472593
Type:
cDNA
Application:
Protein Expression
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Insert length:
1179 bp
Vector type:
Mammalian Expression Vector
Vector backbone:
pPM-C-HA
Resistance Gene:
Kanamycin
Selection Marker:
Neomycin
Promoter:
CMV Promoter
Fusion Tag:
HA tag
Expression:
Stable, Transient
Sequencing Primer:
  • CMV sequencing primer: 5` CGC AAA TGG GCG GTA GGC GTG 3`
Format:
Liquid
Buffer:
10 mM Tris-HCI, 1 mM EDTA, pH 8.0
Storage:
-20 °C
Mouse BCKDHB CRISPR gRNA in Lenti Particles
gRNA PExp, GEEN Lentiviral Vector pLenti-U6-sgRNA-PGK-Neo Ampicillin U6 Promoter unconjugated Stable
Type:
gRNA
Application:
Protein Expression, Genome Editing with Engineered Nucleases
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_199195
Species:
Mouse
Vector type:
Lentiviral Vector
Vector backbone:
pLenti-U6-sgRNA-PGK-Neo
Resistance Gene:
Ampicillin
Selection Marker:
Neomycin
Promoter:
U6 Promoter, PGK Promoter
Expression:
Stable, Transient
Catalog No. ABIN5104925
Datasheet
Catalog No. ABIN5104925
Type:
gRNA
Application:
Protein Expression, Genome Editing with Engineered Nucleases
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_199195
Species:
Mouse
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Vector type:
Lentiviral Vector
Vector backbone:
pLenti-U6-sgRNA-PGK-Neo
Resistance Gene:
Ampicillin
Selection Marker:
Neomycin
Promoter:
U6 Promoter, PGK Promoter
Expression:
Stable, Transient
Components:
Lentiviral particles with an individual gRNA (300 μL) for a specific sequence of Bckdhb
Format:
Viral Particles
Storage:
-80 °C
Rat BCKDHB CRISPR gRNA in Lenti Particles
gRNA PExp, GEEN Lentiviral Vector pLenti-U6-sgRNA-PGK-Neo Ampicillin U6 Promoter unconjugated Stable
Type:
gRNA
Application:
Protein Expression, Genome Editing with Engineered Nucleases
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_019267
Species:
Rat
Vector type:
Lentiviral Vector
Vector backbone:
pLenti-U6-sgRNA-PGK-Neo
Resistance Gene:
Ampicillin
Selection Marker:
Neomycin
Promoter:
U6 Promoter, PGK Promoter
Expression:
Stable, Transient
Catalog No. ABIN5104927
Datasheet
Catalog No. ABIN5104927
Type:
gRNA
Application:
Protein Expression, Genome Editing with Engineered Nucleases
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_019267
Species:
Rat
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Vector type:
Lentiviral Vector
Vector backbone:
pLenti-U6-sgRNA-PGK-Neo
Resistance Gene:
Ampicillin
Selection Marker:
Neomycin
Promoter:
U6 Promoter, PGK Promoter
Expression:
Stable, Transient
Components:
Lentiviral particles with an individual gRNA (300 μL) for a specific sequence of Bckdhb
Format:
Viral Particles
Storage:
-80 °C
Human BCKDHB CRISPR gRNA in Lenti Particles
gRNA PExp, GEEN Lentiviral Vector pLenti-U6-sgRNA-PGK-Neo Ampicillin U6 Promoter unconjugated Stable
Type:
gRNA
Application:
Protein Expression, Genome Editing with Engineered Nucleases
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_000056
Species:
Human
Vector type:
Lentiviral Vector
Vector backbone:
pLenti-U6-sgRNA-PGK-Neo
Resistance Gene:
Ampicillin
Selection Marker:
Neomycin
Promoter:
U6 Promoter, PGK Promoter
Expression:
Stable, Transient
Catalog No. ABIN5104923
Datasheet
Catalog No. ABIN5104923
Type:
gRNA
Application:
Protein Expression, Genome Editing with Engineered Nucleases
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_000056
Species:
Human
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Vector type:
Lentiviral Vector
Vector backbone:
pLenti-U6-sgRNA-PGK-Neo
Resistance Gene:
Ampicillin
Selection Marker:
Neomycin
Promoter:
U6 Promoter, PGK Promoter
Expression:
Stable, Transient
Components:
Lentiviral particles with an individual gRNA (300 μL) for a specific sequence of BCKDHB
Format:
Viral Particles
Storage:
-80 °C
Human BCKDHB cDNA Clone in Bacterial Expression Vector (His-GST)
cDNA Clon Bacterial Expression Vector pPB-His-GST Kanamycin T7 Promoter His-GST Transient
Type:
cDNA
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Vector type:
Bacterial Expression Vector
Vector backbone:
pPB-His-GST
Resistance Gene:
Kanamycin
Promoter:
T7 Promoter
Fusion Tag:
His-GST
Expression:
Transient
Catalog No. ABIN4827182
Datasheet
Catalog No. ABIN4827182
Type:
cDNA
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Insert length:
1179 bp
Vector type:
Bacterial Expression Vector
Vector backbone:
pPB-His-GST
Resistance Gene:
Kanamycin
Promoter:
T7 Promoter
Fusion Tag:
His-GST
Expression:
Transient
Sequencing Primer:
  • GST Forward primer: 5'-CACGTTTGGTGGTGGCGAC3'
  • T7 terminator primer: 5'-GCTAGTTATTGCTCAGCGG-3'
Format:
Liquid
Buffer:
10 mM Tris-HCI, 1 mM EDTA, pH 8.0
Storage:
-20 °C
Human BCKDHB cDNA Clone in Bacterial Expression Vector (His tag)
cDNA Clon Bacterial Expression Vector pPB-N-His Kanamycin T7 Promoter His tag Transient
Type:
cDNA
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Vector type:
Bacterial Expression Vector
Vector backbone:
pPB-N-His
Resistance Gene:
Kanamycin
Promoter:
T7 Promoter
Fusion Tag:
His tag
Expression:
Transient
Catalog No. ABIN4758968
Datasheet
Catalog No. ABIN4758968
Type:
cDNA
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Insert length:
1179 bp
Vector type:
Bacterial Expression Vector
Vector backbone:
pPB-N-His
Resistance Gene:
Kanamycin
Promoter:
T7 Promoter
Fusion Tag:
His tag
Expression:
Transient
Sequencing Primer:
  • T7 promoter primer: 5'-TAATACGACTCACTATAGGG-3'
  • T7 terminator primer: 5'-GCTAGTTATTGCTCAGCGG-3'
Format:
Liquid
Buffer:
10 mM Tris-HCI, 1 mM EDTA, pH 8.0
Storage:
-20 °C
Human BCKDHB cDNA Clone in Bacterial Expression Vector (His-MBP)
cDNA Clon Bacterial Expression Vector pPB-His-MBP Kanamycin T7 Promoter His-MBP Transient
Type:
cDNA
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Vector type:
Bacterial Expression Vector
Vector backbone:
pPB-His-MBP
Resistance Gene:
Kanamycin
Promoter:
T7 Promoter
Fusion Tag:
His-MBP
Expression:
Transient
Catalog No. ABIN4698053
Datasheet
Catalog No. ABIN4698053
Type:
cDNA
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Insert length:
1179 bp
Vector type:
Bacterial Expression Vector
Vector backbone:
pPB-His-MBP
Resistance Gene:
Kanamycin
Promoter:
T7 Promoter
Fusion Tag:
His-MBP
Expression:
Transient
Sequencing Primer:
  • MBP Forward primer: 5'-CGCAGATGTCCGCTTTCTGG-3'
  • T7 terminator primer: 5'-GCTAGTTATTGCTCAGCGG-3'
Format:
Liquid
Buffer:
10 mM Tris-HCI, 1 mM EDTA, pH 8.0
Storage:
-20 °C
Human BCKDHB cDNA Clone in Mammalian Expression Vector (His tag)
cDNA PExp Mammalian Expression Vector pPM-C-His Kanamycin CMV Promoter His tag Stable
Type:
cDNA
Application:
Protein Expression
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Vector type:
Mammalian Expression Vector
Vector backbone:
pPM-C-His
Resistance Gene:
Kanamycin
Selection Marker:
Neomycin
Promoter:
CMV Promoter
Fusion Tag:
His tag
Expression:
Stable, Transient
Catalog No. ABIN4433688
Datasheet
Catalog No. ABIN4433688
Type:
cDNA
Application:
Protein Expression
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
Species:
Human
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Insert length:
1179 bp
Vector type:
Mammalian Expression Vector
Vector backbone:
pPM-C-His
Resistance Gene:
Kanamycin
Selection Marker:
Neomycin
Promoter:
CMV Promoter
Fusion Tag:
His tag
Expression:
Stable, Transient
Sequencing Primer:
  • CMV sequencing primer: 5` CGC AAA TGG GCG GTA GGC GTG 3`
Format:
Liquid
Buffer:
10 mM Tris-HCI, 1 mM EDTA, pH 8.0
Storage:
-20 °C
Mouse BCKDHB ORF Clone in Cloning Vector
ORF Clon Cloning Vector pORF Spectinomycin unconjugated Transient
Type:
ORF
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_199195
Species:
Mouse
Vector type:
Cloning Vector
Vector backbone:
pORF
Resistance Gene:
Spectinomycin
Expression:
Transient
Catalog No. ABIN5733142
Datasheet
Catalog No. ABIN5733142
Type:
ORF
Application:
Cloning
Gene:
Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
NCBI Accession:
NM_199195
Species:
Mouse
Synonyms:
BCKDHB, bckdhb, bckdhb.S, Bckdhb
Insert length:
969 bp
Vector type:
Cloning Vector
Vector backbone:
pORF
Resistance Gene:
Spectinomycin
Expression:
Transient
Sequencing Primer:
  • M13 FP: 5'-CCCAGTCACGACGTTGTAAAACG-3'
    M13 RP: 5'-CAGGAAACAGCTATGAC-3'
Format:
Liquid
Buffer:
10  mM Tris-HCI, 1  mM EDTA,  pH 8.0
Storage:
-20 °C
  • Type
    • Plasmid
    • Primer
  • Supplier
    • antibodies-online
    • OriGene
    • GenScript
    • ProteoGenix
  • Reactivity
    • Human
    • Rat
    • Mouse
  • Application
    • Protein Expression (PExp)
    • Genome Editing with Engineered Nucleases (GEEN)
    • Cloning (Clon)
    • RNA Interference (RNAi)
  • Conjugate
    • Un-conjugated
    • GFP tag
    • His tag
    • Myc-DYKDDDDK Tag
    • HA tag
    • His-GST
    • His-MBP
    • DYKDDDDK Tag
    • RFP tag
  • Vector Backbone
    • pLenti-U6-sgRNA-PGK-Neo
    • pLenti-U6-sgRNA-SFFV-Cas9-2A-Puro
    • pCMV6-Entry
    • pGFP-C-shLenti
    • pGFP-V-RS
    • pORF
    • pPB-His-GST
    • pPB-His-MBP
    • pPB-N-His
    • pPM-C-HA
    • pPM-C-His
    • pRS
    • pCMV6-AC-GFP
    • pCMV6-XL5
    • pCas-Guide
    • pDONR223
    • pRFP-C-RS
    • pcDNA3.1+C-(K)-DYK
  • Vector
    • Mammalian Expression Vector
    • Lentiviral Vector
    • Bacterial Expression Vector
    • Retroviral Vector
    • Cloning Vector
    • Gateway Cloning Vector
  • Insert
    • cDNA
    • ORF
    • shRNA
    • gRNA + Cas9
    • gRNA
  • Type of Oligonucleotide
    • siRNA Oligo
  • Bacterial Resistance
    • Ampicillin
    • Kanamycin
    • Chloramphenicol
    • Spectinomycin
  • Expression Type
    • Transient
    • Stable
  • Selectable Marker
    • Neomycin
    • Puromycin
  • Promoter
    • U6 Promoter
    • CMV Promoter
    • T7 Promoter
    • PGK Promoter
    • SFFV Promoter
    • Enhanced CMV Promoter
  • Format
    • Lyophilized
    • Liquid
    • Viral Particles

Synonyms and alternative names related to BCKDHB

  • branched chain keto acid dehydrogenase E1, beta polypeptide (BCKDHB)
  • branched chain keto acid dehydrogenase E1 subunit beta (BCKDHB)
  • branched chain keto acid dehydrogenase E1, beta polypeptide (bckdhb)
  • branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog (bckdhb.S)
  • branched chain keto acid dehydrogenase E1 subunit beta (Bckdhb)
  • branched chain ketoacid dehydrogenase E1, beta polypeptide (Bckdhb)
  • BCKDHB
  • dJ279A18.1
  • E1B
  • zgc:158777

Gene-IDs for different species

Protein level used designations for BCKDHB

  • 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
  • branched chain keto acid dehydrogenase E1, beta polypeptide (maple syrup urine disease)
  • mitochondrial branched-chain alpha-keto acid dehydrogenase E1-beta subunit
  • branched chain keto acid dehydrogenase E1, beta polypeptide
  • branched chain keto acid dehydrogenase E1 beta polypeptide
  • branched chain keto acid dehydrogenase E1 beta-like
  • 2-oxoisovalerate dehydrogenase beta subunit
  • BCKDE1B
  • BCKDH E1-beta
  • branched chain keto acid dehydrogenase E1 beta
  • branched-chain alpha-keto acid dehydrogenase E1 component beta chain
  • E1b-beta subunit of the branched-chain complex
  • branched chain alpha-ketoacid dehydrogenase E1-beta subunit
Other products related to BCKDHB such as antibodies, ELISA kits and high-purity proteins are available on our partner website antibodies-online.com
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